Clinical course
・ 転移性肝腫瘍が第1に疑われ、全身の検索 が行われたが異常なし。
・ 肝腫瘍の針生検が行われ、病理組織診断は Epithelioid hemangioendothelioma (EHE) of the liver(疑い)
・ 生体肝移植目的にて当院紹介
診断:EHE of the liver
・ Low-grade malignant vascular tumor
・ Mean age: 41.7years
・ Male to Female ratio 2:3
・ Clinical manifestions: nonspecific
・ 1-year and 5-year survival
_ after resection: 100%, 75%
_ after transplantation: 96%, 54.5%
_ no treatment: 39.3%, 4.5%
EHE of the liver
・ Multifocal nodular pattern (more common)
・ Diffuse pattern
・ Located at periphery
・ Calcification:20%
・ Capsular retraction:25%
_ due to occlusion of peripheral bile ducts
・ Compensatory hypertrophy
Target like enhancement
・ Nonenhancing central part
_ necrosis, fibromyxoid stroma
・ Enhancing inner rim
_ hyperemia
・ Nonenhancing outer rim
_ avascular zone